Movement Disorders (revue)

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Acute reversible parkinsonism in Epstein–Bbarr virus–related encephalitis lethargica‐like illness

Identifieur interne : 003605 ( Main/Exploration ); précédent : 003604; suivant : 003606

Acute reversible parkinsonism in Epstein–Bbarr virus–related encephalitis lethargica‐like illness

Auteurs : Petia S. Dimova [Bulgarie] ; Veneta Bojinova [Bulgarie] ; Dimitar Georgiev [Bulgarie] ; Ivan Milanov [Bulgarie]

Source :

RBID : ISTEX:C98DE8CCF465711886A7D3231809BBB545E80419

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Abstract

A 10‐year‐old boy presented with fever, headache, vomiting, and hypersomnolence. An akinetic–rigid syndrome with tremor, dysphagia, dysphonia, and sialorrhea, as well as pyramidal signs, developed. Slightly elevated protein content was found in the cerebrospinal fluid and serological investigations were suggestive of a primary Epstein–Barr virus infection. Magnetic resonance imaging (MRI) showed massive bilateral hyperintense striatal and punctiform periventricular lesions. After 2‐month treatment with steroids and antiparkinsonian drugs, all features resolved without sequelae. Control MRI demonstrated only minimal residual lesions in both putamina. Strongly resembling the encephalitis lethargica‐like syndrome, this case is an unusual presentation of parainfectious acute disseminated encephalitis. © 2005 Movement Disorder Society

Url:
DOI: 10.1002/mds.20742


Affiliations:


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Le document en format XML

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<div type="abstract" xml:lang="en">A 10‐year‐old boy presented with fever, headache, vomiting, and hypersomnolence. An akinetic–rigid syndrome with tremor, dysphagia, dysphonia, and sialorrhea, as well as pyramidal signs, developed. Slightly elevated protein content was found in the cerebrospinal fluid and serological investigations were suggestive of a primary Epstein–Barr virus infection. Magnetic resonance imaging (MRI) showed massive bilateral hyperintense striatal and punctiform periventricular lesions. After 2‐month treatment with steroids and antiparkinsonian drugs, all features resolved without sequelae. Control MRI demonstrated only minimal residual lesions in both putamina. Strongly resembling the encephalitis lethargica‐like syndrome, this case is an unusual presentation of parainfectious acute disseminated encephalitis. © 2005 Movement Disorder Society</div>
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